gene: bckd-1B [Browse genome (BioProject PRJNA13758)] [Search on AGR]
Caenorhabditis elegans Predicted to enable catalytic activity. Involved in positive regulation of fatty acid biosynthetic process and positive regulation of nematode larval development. Predicted to be located in mitochondrion. Predicted to be part of mitochondrial alpha-ketoglutarate dehydrogenase complex. Human ortholog(s) of this gene implicated in maple syrup urine disease. Is an ortholog of human BCKDHB (branched chain keto acid dehydrogenase E1 subunit beta).