hex-1

Caenorhabditis elegans

Enables beta-N-acetylhexosaminidase activity. Involved in carbohydrate metabolic process. Predicted to be located in lysosome and membrane. Expressed in coelomocyte and pharyngeal neurons. Human ortholog(s) of this gene implicated in Sandhoff disease; Tay-Sachs disease; and spinal muscular atrophy. Is an ortholog of human HEXA (hexosaminidase subunit alpha) and HEXB (hexosaminidase subunit beta).