Predicted to be involved in maturation of SSU-rRNA from tricistronic rRNA transcript (SSU-rRNA, 5.8S rRNA, LSU-rRNA). Predicted to be located in nucleus. Human ortholog(s) of this gene implicated in Diamond-Blackfan anemia 14 with mandibulofacial dysostosis. Is an ortholog of human TSR2 (TSR2 ribosome maturation factor).
Is affected by Cbr-spr-4 based on RNA-seq studies. Is predicted to encode a protein with the following domain: Pre-rRNA-processing protein TSR2. Is an ortholog of C. elegans Y51H4A.15.